Arrhythmogenic right ventricular cardiomyopathy 2012: diagnostic challenges and treatment.

Assessing the significance of pathogenic mutations and autopsy findings in the light of 2010 arrhythmogenic right ventricular cardiomyopathy diagnostic criteria: a clinical challenge.

Diagnostic Dilemmas: Overlapping Features of Brugada Syndrome and Arrhythmogenic Right Ventricular Cardiomyopathy

Arrhythmogenic right ventricular cardiomyopathy (ARVC) and Brugada syndrome are distinct clinical entities which diagnostic criteria exclude their coexistence in individual patients. ARVC is a myocardial disorder characterized by fibro-fatty replacement of the myocardium and ventricular arrhythmias. In contrast, the Brugada syndrome has long been considered a functional cardiac disorder: no gro...

Arrhythmogenic right ventricular cardiomyopathy mimics: clinical impact of cardiovascular magnetic resonance

Background The diagnosis of arrhythmogenic right ventricular cardiomyopathy (ARVC) often relies on CMR to assess volumes, function and myocardial tissue characterization for detection of both fat and fibrosis in vivo. Clinical suspicious of ARVC often leads to CMR evaluation to refute or confirm a diagnosis. However, various diseases may mimic ARVC causing diagnostic dilemmas. We used CMR to ex...

Improve of arrhythmogenic right ventricular cardiomyopathy/dysplasia evaluation by magnetic resonance using ventricular arrhythmia suppression with intravenous lidocaine

Background New recommendations from task force criteria for the diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) include regional right ventricle (RV) akinesia or dyskinesia or dyssynchronous RV contraction associated to RV dilatation or RV dysfunction evaluated by magnetic resonance imaging (MRI) as major diagnostic criteria. However the frequent presentation of ...

Correlation of cardiac magnetic resonance imaging and electrophysiology study findings among patients with frequent premature ventricular contractions

Despite inclusion in the diagnostic criteria for arrhythmogenic right ventricular cardiomyopathy, this study of 87 consecutive patients with isolated frequent LBBBmorphology PVCs and high PVC burden (mean 19%) demonstrated only a rare association with CMR diagnostic criteria for ARVC, no cases of ARVC diagnosis, no association of minor wall motion abnormalities (hypokinesis) with markers of ARV...